Case Report

Rapidly involuting congenital hemangioma associated with Kasabach-Merritt Syndrome

Rosalia Ballona*, Jean Zevallos and Jeanette Núñez

Published: 17 May, 2021 | Volume 4 - Issue 1 | Pages: 050-052

Background: Rapidly involuting congenital hemangioma (RICH) is a rare vascular tumor that is present at birth and involutes during the first year of life. Kasabach-Merritt syndrome (KMS) is a complication of some vascular tumors such as kaposiform hemangioendothelioma and tufted angioma associated with thrombocytopenia and coagulopathy.

Results: The case of a 2-month-old infant with a diagnosis of RICH with thrombocytopenia and coagulation disorder, successfully treated with surgical excision without complications or recurrence is presented.

Conclusion: The association between RICH and KMS is rare. Histopathological study, immunohistochemistry and ultrasound findings are important for the diagnosis.

Brief summary: This report covers the rare association between rapidly involuting congenital hemangioma and Kasabach-Merritt syndrome in a 2-months-old female infant.

Read Full Article HTML DOI: 10.29328/journal.japch.1001032 Cite this Article Read Full Article PDF


Rapidly involuting congenital hemangioma; Kasabach-Merritt Syndrome


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